Congenital fibrinogen deficiency is a rare autosomal disorder of coagulation with unknown prevelance and diverse range of bleeding phenotypes. Only few cases of CNS bleeding in paediatric patients with fibrinogen deficiency are reported and are related with increased morbidity and mortality. The perioperative management of an infant with an acute epidural hematoma after minor head injury, with previous unknown congenital fibrinogen deficiency, is presented.

Anaesthetic approach to epidural hematoma, after minor head trauma in an infant with previously unknown fibrinogen deficiency