Background and Aims
Chiari type II malformation a congenital malformation of the spine and a small posterior fossa in form of myelomeningocele, as well as other brain anomalies. Associated structural malformations and sequelae, such as cranial nerve palsies, neurogenic bladder, hydrocephalus and scoliosis. 

Method
IVF donor egg and sperm pregnancy in a lesbian couple. It was an uneventful pregnancy up until 20 weeks gestation, when at a routine antenatal scan revealed a Chiari type II malformation with open myelomeningocele. Baby boy was born in good condition by an elective LSCS at 37+1 weeks, weighing 2970 grams. Myelomeningocele was successfully repaired on day 1 of life. On post-operative imaging it was noted baby had moderately enlarged lateral and third ventricles, with malformation of corpus callosum and absence of septum pellucidum. By 2 weeks of age a ventriculo-peritoneal shunt was inserted due to bulging fontanelle and irritability. 

Results
Baby was referred to Community Paediatric clinic at 6 months of age for neurodevelopmental assessment. He was well and no longer requiring intermittent catheterisation. He was suffering with sleep apnoeas, snoring and excessive drooling, as well as cow’s milk protein intolerance and reflux. Neurological examination was normal. However, he completely lacked head control. He had a good eye contact, normal hearing and a social smile. 

Conclusion
The antenatal ultrasound scan remains the main means of diagnosis and initial assessment of this foetal malformation, which is followed by thorough postnatal evaluation with MRI scan.

0327 - A CASE REPORT OF ANTENATALLY DIAGNOSED CHIARI TYPE II MALFORMATION