Title: A Review of Outcomes in Cochlear Implanted Children with Mitochondrial Hearing Loss.
Objectives:
Mitochondrial diseases are chronic (long-term), genetic, often inherited disorders that occur when mitochondria fail to produce enough energy for the body to function properly. The aim of the study was to review the outcomes of several children with Mitochondrial hearing loss who had been implanted in the first four years of life at the West of England Hearing Implant Programme.
Methods:
The children's progress was tracked both quantitatively and qualitatively. A questionnaire was used with the parents to ascertain the impact on the child's quality of life.
Outcomes:
It is proposed that the data for each child will be analysed. It will explore whether cochlear implantation has enhanced the lives of the children.
Conclusion:
There is a huge variety in the symptoms and severity associated with Mitochondrial disease. Given the heterogeneity of the disease, it is very difficult to predict an individual’s listening and communication development. The children's experiences, both positive and more challenging, will be discussed. This will include the impact on their quality of life since initial tuning.

Title: A Review of Outcomes in Cochlear Implanted Children with Mitochondrial Hearing Loss.
**Objectives:**
Mitochondrial diseases are chronic (long-term), genetic, often inherited disorders that occur when mitochondria fail to produce enough energy for the body to function properly. The aim of the study was to review the outcomes of several children with Mitochondrial hearing loss who had been implanted in the first four years of life at the West of England Hearing Implant Programme.
**Methods:**
The children's progress was tracked both quantitatively and qualitatively. A questionnaire was used with the parents to ascertain the impact on the child's quality of life.
**Outcomes:**
It is proposed that the data for each child will be analysed. It will explore whether cochlear implantation has enhanced the lives of the children.
**Conclusion:**
There is a huge variety in the symptoms and severity associated with Mitochondrial disease. Given the heterogeneity of the disease, it is very difficult to predict an individual’s listening and communication development. The children's experiences, both positive and more challenging, will be discussed. This will include the impact on their quality of life since initial tuning.

A Review of Outcomes in Cochlear Implanted Children with Mitochondrial Hearing Loss

It is with great pleasure and enthusiasm, that on behalf of the Cochlear Implant centers of the Radboud UMC in Nijmegen and Erasmus MC Sophia Children’s Hospital in Rotterdam to invite you to attend the 16th European Symposium on Pediatric Cochlear Implantation to Rotterdam, the Netherlands in 2023.

Yours sincerely, on behalf of the CI Centers at Radboud UMC and Erasmus MC,